Survey of Ophthalmology
Volume 47, Issue 4 , Pages 368-374, July 2002

Malignant Ectomesenchymoma of the Orbit in a Child:

Case Report and Review of the Literature

  • Peter Paikos, MD

      Affiliations

    • Departments of Ophthalmology, Agia Sofia Children's Hospital, Athens, Greece
    • Corresponding Author InformationReprint address: Peter Paikos, MD, AGIA SOFIA Children's Hospital, Dept. of Ophthalmology, Thivon and Livadias str., Goudi, 11527, Athens, Greece
    • ,
  • Miltiadis Papathanassiou, MD

      Affiliations

    • Departments of Ophthalmology, Agia Sofia Children's Hospital, Athens, Greece
    • ,
  • Kalliopi Stefanaki, MD

      Affiliations

    • Departments of Pathology, Agia Sofia Children's Hospital, Athens, Greece
    • ,
  • Maria Fotopoulou, MD

      Affiliations

    • Departments of Ophthalmology, Agia Sofia Children's Hospital, Athens, Greece
    • ,
  • Spyropoulos Grigorios, MD

      Affiliations

    • Departments of Ophthalmology, Agia Sofia Children's Hospital, Athens, Greece
    • ,
  • Foteini Tzortzatou, MD

      Affiliations

    • Departments of Oncology, Agia Sofia Children's Hospital, Athens, Greece

MILTON BONIUK AND STEFAN SEREGARD, EDITORS

Abstract 

Malignant ectomesenchymoma is a rare soft tissue tumor of childhood composed of both mesenchymal and neuroectodermal elements. Reported sites of origin are head and neck, abdomen, perineum, scrotum, and extremities. A new case of an orbital ectomesenchymoma in a 7-year-old boy is presented. The clinical picture of the tumor, radiological findings, and its histopathologic and immunohistochemical characteristics are described. The patient was successfully treated with combined surgical resection and chemotherapy. All the other reported cases of malignant ectomesenchymoma with various sites of origin are also reviewed.

Keywords:  ectomesenchymoma, immunohistochemistry, orbit, soft tissue tumors

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PII: S0039-6257(02)00313-2

Survey of Ophthalmology
Volume 47, Issue 4 , Pages 368-374, July 2002

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